TY - JOUR
T1 - Clear cell sarcoma-A review
AU - Ibrahim, Rami Mossad
AU - Steenstrup Jensen, Signe
AU - Juel, Jacob
PY - 2018/12/1
Y1 - 2018/12/1
N2 - Clear cell sarcoma (CCS) previously known as malignant melanoma (MM) of the soft tissue, although, similar in morphology to MM, contemporary histopathologic and cytogenetic techniques have made this diagnosis obsolete, as it is now possible to distinguish between CCS and MM. CCS is often diagnosed in young adults with median age of 25 years. Overall mortality is generally poor, and the 5-year survival is between 40 and 60%. Hence, early diagnosis and radical surgery are key in the treatment of this extremely rare malignancy of the soft tissue comprising only about 1% of all sarcomas. This article present an overview of this rare malignancy.
AB - Clear cell sarcoma (CCS) previously known as malignant melanoma (MM) of the soft tissue, although, similar in morphology to MM, contemporary histopathologic and cytogenetic techniques have made this diagnosis obsolete, as it is now possible to distinguish between CCS and MM. CCS is often diagnosed in young adults with median age of 25 years. Overall mortality is generally poor, and the 5-year survival is between 40 and 60%. Hence, early diagnosis and radical surgery are key in the treatment of this extremely rare malignancy of the soft tissue comprising only about 1% of all sarcomas. This article present an overview of this rare malignancy.
KW - Clear cell sarcoma
KW - Malignant melanoma of the soft tissue
KW - Sarcoma
KW - Treatment of clear cell sarcoma
UR - http://www.scopus.com/inward/record.url?scp=85053076287&partnerID=8YFLogxK
U2 - 10.1016/j.jor.2018.08.039
DO - 10.1016/j.jor.2018.08.039
M3 - Review article
C2 - 30210202
SN - 0972-978X
VL - 15
SP - 963
EP - 966
JO - Journal of Orthopaedics
JF - Journal of Orthopaedics
IS - 4
ER -