TY - JOUR
T1 - Rupture of an abdominal aortic aneurysm in a young man with Marfan Syndrome
AU - Pedersen, Maria Weinkouff
AU - Huynh, Khiem Dinh
AU - Baandrup, Ulrik Thorngren
AU - Nielsen, Dorte Guldbrand
AU - Andersen, Niels Holmark
N1 - Copyright © 2018 Elsevier Inc. All rights reserved.
PY - 2018/4
Y1 - 2018/4
N2 - Abdominal aortic aneurysms are very rare in Marfan syndrome. We present a case with a young non-smoking and normotensive male with Marfan syndrome, who developed an infrarenal abdominal aortic aneurysm that presented with rupture to the retroperitoneal cavity causing life-threatening bleeding shock. The patient had acute aortic surgery and survived. Five months before this incident, the patient had uneventful elective aortic root replacement (a.m David) due to an enlarged aortic root. At that time, his abdominal aorta was assessed with a routine ultrasound scan that showed a normal sized abdominal aorta. This documents that the aneurysm had evolved very rapidly despite young age, and absence of risk factors.
AB - Abdominal aortic aneurysms are very rare in Marfan syndrome. We present a case with a young non-smoking and normotensive male with Marfan syndrome, who developed an infrarenal abdominal aortic aneurysm that presented with rupture to the retroperitoneal cavity causing life-threatening bleeding shock. The patient had acute aortic surgery and survived. Five months before this incident, the patient had uneventful elective aortic root replacement (a.m David) due to an enlarged aortic root. At that time, his abdominal aorta was assessed with a routine ultrasound scan that showed a normal sized abdominal aorta. This documents that the aneurysm had evolved very rapidly despite young age, and absence of risk factors.
KW - Aortic Aneurysm, Abdominal/diagnostic imaging
KW - Aortic Rupture/diagnostic imaging
KW - Aortography/methods
KW - Biopsy
KW - Blood Vessel Prosthesis Implantation
KW - Computed Tomography Angiography
KW - Humans
KW - Male
KW - Marfan Syndrome/complications
KW - Treatment Outcome
KW - Ultrasonography
KW - Young Adult
UR - http://www.scopus.com/inward/record.url?scp=85043520875&partnerID=8YFLogxK
U2 - 10.1016/j.avsg.2017.10.024
DO - 10.1016/j.avsg.2017.10.024
M3 - Journal article
C2 - 29421423
SN - 0890-5096
VL - 48
SP - 252.e5-252.e8
JO - Annals of Vascular Surgery
JF - Annals of Vascular Surgery
ER -