Clear cell sarcoma-A review

Rami Mossad Ibrahim, Signe Steenstrup Jensen, Jacob Juel

Research output: Contribution to journalReview articlepeer-review

21 Citations (Scopus)
252 Downloads (Pure)


Clear cell sarcoma (CCS) previously known as malignant melanoma (MM) of the soft tissue, although, similar in morphology to MM, contemporary histopathologic and cytogenetic techniques have made this diagnosis obsolete, as it is now possible to distinguish between CCS and MM. CCS is often diagnosed in young adults with median age of 25 years. Overall mortality is generally poor, and the 5-year survival is between 40 and 60%. Hence, early diagnosis and radical surgery are key in the treatment of this extremely rare malignancy of the soft tissue comprising only about 1% of all sarcomas. This article present an overview of this rare malignancy.

Original languageEnglish
JournalJournal of Orthopaedics
Issue number4
Pages (from-to)963-966
Number of pages4
Publication statusPublished - 1 Dec 2018


  • Clear cell sarcoma
  • Malignant melanoma of the soft tissue
  • Sarcoma
  • Treatment of clear cell sarcoma


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